Provided below are ELISA kits targeting leucine rich pentatricopeptide repeat containing, a human protein encoded by LRPPRC. This protein is 1394 amino acids long with a reported mass of 157.9 kDa. This is reported to be a nuclear and mitochondrial protein. There is a noted implication in Leigh syndrome French-Canadian type. Other alias names for this protein include: leucine-rich PPR motif-containing protein mitochondrial, 130 kDa leucine-rich protein, LRP 130, leucine-rich PPR-motif containing, CLONE-23970, GP130, and LRP130.