Anti-DHTKD1 Antibody, Rabbit Polyclonal AAA254813 from AAA Biotech, LLC

Description

DHTKD1, a part of 2-ketoadipic acid dehydrogenase complex, is involved in lysine and tryptophan catabolism. Mutations in DHTKD1 block the metabolic pathway and cause 2-aminoadipic and 2-oxoadipic aciduria (AMOXAD), an autosomal recessive inborn metabolic disorder. The mutations in dehydrogenase E1 and transketolase domain-containing 1 (DHTKD1), a mitochondrial protein encoding gene, could cause neurological abnormalities

Product Specs
ItemAnti-DHTKD1 Antibody, Rabbit Polyclonal
CompanyAAA Biotech, LLC
Price $380.00Supplier Page View Company Product Page
Catalog NumberAAA254813
StorageThis antibody can be stored at 2-8 degree C for one month without detectable loss of activity. Antibody products are stable for twelve months from date of receipt when stored at -20 degree C to -80 degree C. Preservative-Free. Avoid repeated freeze-thaw cycles
ReactivityHuman
TypeAntibody
TargetDHTKD1
Quantity0.1 mL, 5x0.1 mL, 4x0.1 mL, 2x0.1 mL, 3x0.1 mL
ClonalityPolyclonal
FormatLiquid; 0.2um filtered solution in PBS
IsotypeRabbit IgG
ApplicationsIP (Immunoprecipitation), WB (Western Blot)
HostRabbit
Molecular Weight103,077 Da
PurityProtein A & Antigen Affinity
NCBI Full Gene Namedehydrogenase E1 and transketolase domain containing 1
NCBI Gene AliasesOADC-E1, AMOXAD, E1a, AAKAD, OADH-E1, CMT2Q
Conjugate/TagUnconjugated