The MCCC1 Polyclonal Antibody from MyBioSource.com is a Rabbit Polyclonal antibody to MCCC1, and methylcrotonyl-CoA carboxylase subunit 1. This antibody recognizes Human, and Mouse antigen. The MCCC1 Polyclonal Antibody has been shown to work in the following applications: Western Blot.
Description
This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism