BCKDHB ELISA kits are immunoassay tools for the measurement of the protein branched chain keto acid dehydrogenase E1 subunit beta, which is encoded by the BCKDHB gene in humans. Functionally, this protein is known to be involved in the metabolism of lipids. The canonical protein structure is reported to have an amino acid sequence of 392 residues and a mass of 43.1 kDa. It is known to be localized in the mitochondria. As many as 2 protein isoforms have been reported. The BCKDHB gene has been associated with the disease, Maple syrup urine disease. Other alias names for this target include BCKDH E1-beta, E1B, 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, E1b-beta subunit of the branched-chain complex, and BCKDE1B.
There are BCKDHB ELISA kits that can detect a target at concentrations as low as 31.25 pg/mL and as high as 20 ng/mL. Click on the products below for more detailed ELISA kit information, such as target reactivity and assay sensitivity.