Anti-BCKDHB antibodies are used in the immunodetection of the protein branched chain keto acid dehydrogenase E1 subunit beta. In humans, the canonical protein has a reported length of 392 amino acid residues and a mass of 43.1 kDa. Its subcellular localization is in the mitochondria. Up to 2 different isoforms have been reported for this protein. It is notably widely expressed in many tissue types. BCKDHB is known to be involved with the metabolism of lipids. The BCKDHB gene has been associated with the disease, Maple syrup urine disease. Synonyms for this target antigen include BCKDH E1-beta, E1B, 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, E1b-beta subunit of the branched-chain complex, and BCKDE1B. BCKDHB gene orthologs have been reported in the mouse, rat, bovine, frog, zebrafish, chimpanzee and chicken species. A number of BCKDHB antibodies have been mentioned in research publications and have associated citations. Western Blot is a widely used application for these antibodies. ELISA, Immunofluorescence, and Immunohistochemistry are also common applications.